Table 1

Demographics and characteristics

VariableCounts (percentages)
Sex
Male14 (47%)
Female16 (53%)
Age at diagnosis (years)*6.5 (0.7–16.7)
Location
Femur only14 (47%)
Humerus only8 (27%)
Tibia only5 (17%)
Tibia+femur2 (7%)
Fibula1 (3%)
Additional skeletal lesions
Skull/maxillofacial5 (17%)
Pelvis4 (13%)
Vertebrae4 (13%)
Ribs/sternum2 (7%)
Clavicle1 (3%)
Classification
Unifocal18 (60%)
Multifocal12 (40%)
Radiographs
Fractures4 (13%)
Lytic lesions22 (73%)
Immunopathology
CD1a+23 (77%)
CD68+7 (23%)
CD207+19 (63%)
S100+12 (40%)
  • *Data are presented with median (range).